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Friday, September 24, 2010

Panniculitis Reaction Pattern

PANNICULITIS     View detailed histological descriptions here

As the name suggests panniculitis is inflammation of the fat layer of the skin.  As it is so deep you can surmise that the lesions are going to present as smooth, red and inflamed lesions without any epidermal involvement.   The commonest one you are going to come across is erythema nodosum and clinically it is going to present as tender painful nodules on the anterior shins., occasionally also on the extensor surfaces of the arms but primarily on the shins, with a little bit of surrounding bruising.  The other disorder you will see will be erythema induratum or nodular vasculitis.  This tends to affect the calves primarily and it may present even as an ulcerated lesion.  Other forms of panniculitis are relatively rare.  You may see pancreatic panniculitis where someone has an inflamed pancreas or pancreatic cyst and pancreatic enzymes leak into the circulation and cause damage to the fat lobules.  Lastly there may be a lupus panniculitis.  It will present in any part of the body but again particularly on the legs and extensor surfaces of the upper arms, as an indurated plaque.  There may or may not be overlying skin involvement with lupus.  Another rare presentation would be cold injury to the skin which tends to occur over fatty areas which insulate the skin, particularly seen on horse riders on the buttocks or in young premature neonates.

As we said this is the commonest presentation of panniculitis that you are likely to see in dermatological practice.  It characteristically follows a streptococcal throat infection or women coming off the contraceptive pill.  It also can be a manifestation of underlying sarcoidosis and it is prudent always to do a chest X-ray.  Histologically the picture that you will see is a septal panniculitis because of its involvement of the vessels that run in the septa between the lobules. Usually there is no necrosis of the lobule itself.  In an acute phase you will see neutrophils in the septum but in the chronic phase generally mononuclear cells and occasionally granulomatous inflammation.  Erythema nodosum can also be seen with inflammatory bowel disease and rarely after infections such as Coccidioidomycosis and Yersinia infection.  There is a chronic form of erythema nodosum that may show a granulomatous histology in the septa with fibrotic lesions.

Pancreatic panniculitis is a lobular panniculitis.  The released pancreatic enzymes attack the liver lobules and destroy them.  There are lymphocytes, foam histiocytes and multinucleated giant cells and the fat necrosis leaves ghost like fat cells, sometimes with deposits of calcium cells.

Again there is necrosis of the fat lobule and there may be fibrous rims around the fat and nodular lymphoid infiltrates.  Occasionally this is mistaken for a subcutaneous lymphoma. Sometimes the overlying epidermis will show the typical features of discoid lupus and the dermis may be sclerotic.

Erythema induratum (nodular vasculitis)   View Clinical    is another cause of red nodules, but they typically occur in the calf and at one stage were thought to represent a tuberculid, in other words an idiopathic reaction to the tuberculin or tuberculosis organism.  Most cases nowadays are usually idiopathic.  Occasionally in this condition you will get ulceration and also a lobular  granulomatous panniculitis with a mixed infiltrate including lymphocytes, histiocytes, plasma cells and giant cells.  Occasionally caseous necrosis will occur and there may be a vasculitis involving the arteries or small veins.  Polyarteritis nodosa has been considered as a significant differential of erythema induratum.

Subcutaneous fat necrosis of the newborn is really quite a rare condition where there are indurated subcutaneous nodules.  Generally this is self limited and they sometimes suffer from hypercalcaemia.  Histologically you get characteristic needle shaped clefts within the fat cells and as well as the fat necrosis, the granulomatous infiltrate and sometimes calcification reflecting the hypercalcaemia.

This condition is not uncommon.  We see it regularly in the elderly particularly beginning on the medial aspects of the ankles and gradually encircling the ankle. The skin is indurated, thickened and sometimes tender. There is usually associated venous insufficiency and stasis dermatitis and this is reflected in the epidermal changes, but there is fat necrosis, marked sclerosis with collagen deposition and lymphocytic infiltrates into the fat tissue in a lobular pattern.

Another rare but characteristic histologically form of panniculitis is cytophagic histiocytic panniculitis.  This again is a lobular panniculitis but it is characterised by bean bag cells which are histiocytes that are full of  engulfed  inflammatory cells and erythrocytes.  This condition may follow infection or can be induced by lymphoma.